Takayasu’s arteritis (TA) is a chronic large-vessel vasculitis of unknown etiology primarily affecting young women of Asian descent. The early manifestations are often followed by vascular bruits, hemiparesis, retinopathy due to localized ischemia of involved vessels. Depending on the degree, various neurologic manifestations also can be observed. Amongst them, headache is the most common neurologic presentation in TA patients. Since the clinical manifestations in pediatric patients are less specific than in adults, diagnosis of TA is challenging without typical localized ischemic symptoms. In this report, we discuss a case of an 8-year-old girl diagnosed as TA, who initially presented no typical vascular symptom and only with vague symptoms: headache, weight loss, febrile sense.