Abstract

Tolosa-Hunt syndrome is characterized by severe unilateral headaches with ophthalmoplegia caused by granulomatous inflammation in the cavernous sinus. Idiopathic hypertrophic cranial pachymeningitis is a rare disorder, which is caused by chronic progressive inflammation and thickening of dura mater and characterized by headache, multiple cranial nerve palsy, ataxia and seizure. Both diseases have similar pathophysiology in that inflammation, but the case reports that combined with two disease entities are rare. Thus we report a case of idiopathic hypertrophic cranial pachy- meningitis presented with Tolosa-Hunt syndrome.